ISSN: 1899-0967
Polish Journal of Radiology
Established by prof. Zygmunt Grudziński in 1926 Sun
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2018
vol. 83
 
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abstract:
Case report

Herlyn-Werner-Wunderlich syndrome – a rare genitourinary anomaly in females: a series of four cases

Mohd Ilyas, Insha Khan, Cimona L. Saldanha

© Pol J Radiol 2018; 83: e306-e310
Online publish date: 2018/06/20
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We present case series of four patients with an important syndrome known as Herlyn-Werner-Wunderlich syndrome. Herlyn-Werner-Wunderlich syndrome is a rare congenital anomaly characterised by uterus didelphys with blind hemivagina and ipsilateral renal agenesis. It usually presents after menarche with progressive pelvic pain during menses secondary to haematocolpos. Awareness is necessary to diagnose and treat this disorder properly before complications occur. Magnetic resonance imaging is the preferred modality for the delineation of uterine malformation. When renal anomalies are encountered, a screening should also be made for congenital abnormalities of the reproductive tract and vice versa.
keywords:

uterus didelphys, obstructed hemivagina, renal agenesis, haematometra, haematocolpos

references:
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Wu TH, Wu TT, Ng YY, et al. Herlyn-Werner-Wunderlich syndrome consisting of uterine didelphys, obstructed hemivagina and ipsilateral renal agenesis in a newborn. Pediatr Neonatol 2012; 53: 68-71. 
Jeong JH, Kim YJ, Chang CH, Choi HI. A case of Herlyn-Werner- Wunderlich syndrome with recurrent hematopyometra. J Womens Med 2009; 2: 77-79.
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Angotti R, Molinaro F, Bullota AL, et al. Herlyn-Werner-Wunderlich syndrome: An “early” onset case report and review of literature. Int J Surg Case Report 2015; 11: 59-63.
Park NH, Park HJ, Park CS, Park SI. Herlyn-Werner-Wunderlich syndrome with unilateral hemivaginal obstruction, ipsilateral renal agenesis and contralateral renal thin GBM disease: A case report with radiological follow up. J Korean Soc Radiol 2010; 62: 383-388.
 
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